Laparoscopic Gonadectomy in 46,xy Gonadal Dysgenesis
نویسنده
چکیده
We reported a case of a 17 year-old female, who presented with primary amenorrhea. She had normal female external genitalia and a 46,XY karyotype. Hormone profiles and laparoscopic findings confirmed a diagnosis of 46,XY gonadal dysgenesis (Swyer syndrome). Prophylactic gonadectomy was performed laparoscopically to prevent the risk of malignant germ cell tumor. Current management of this rare syndrome was reviewed. Chiang Mai Med J 2007;46(1):39-43.
منابع مشابه
Laparoscopic Gonadectomy of Streak Gonads within the Inguinal Canals in a Patient with Xy Partial Gonadal Dysgenesis
A 33-year-old phenotypic female presented with primary amenorrhea. The physical examination revealed no breast development, scanty axillary and pubic hair, normal female external genitalia, and a short blind vagina. The findings of magnetic resonance imaging, karyotyping, and hormonal examinations supported the diagnosis of XY partial gonadal dysgenesis. Laparoscopic surgery showed that spermat...
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تاریخ انتشار 2007